Introduction: Primary central nervous system vasculitis (PCNSV) is a rare inflammatory arteriopathy confined to the brain, spinal cord, and leptomeninges. Because of its nonspecific presentation ...

is another condition that can cause multifocal CNS pathology, including visual loss, and can thus mimic Susac syndrome. BRAO is not a feature of PCNSL, however, and brain lesions in PCNSL are ...